SUOX

SUOX (Sulfite Oxidase): SUOX encodes sulfite oxidase, an enzyme vital for the metabolism of sulfur-containing amino acids. It catalyzes the final step in the degradation of cysteine and methionine, converting sulfite to sulfate, which is excreted in the urine. Deficiencies in SUOX activity lead to sulfite accumulation, resulting in neurological damage and physical abnormalities, a condition known as sulfite oxidase deficiency. This highlights the enzyme's essential role in amino acid metabolism and the prevention of neurotoxicity associated with sulfite accumulation.